Management of Amelogenesis Imperfecta: Report of Three Cases
نویسندگان
چکیده
Amelogenesis Imperfecta (AI) is a genetic disease affecting primary and permanent tooth enamel. The incidence varies between 1:700 to 1:4000. The clinical findings include enamel defects, tooth sensitivity, poor dental aesthetics, reduced vertical dimension, dentin dysplasia, and pulpal calcification. Effective treatment planning should incorporate numerous factors such as the patient’s age, disease type and severity, and general oral condition. Over time, severe tissue destruction may occur, and therefore, it is important to begin treatment as early as possible. The present case report describes patients diagnosed with three types of Al: hypoplastic, hypocalcified, and hypomaturation.
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Amelogenesis Imperfecta with Taurodontism, Microdontia, and Minor Thalassemia: A Case Report
Amelogenesis imperfecta is a group of genetic disorders that affects both the morphology and quality of tooth structure. Although the disease entity is primarily associated with abnormalities of dental and oral structures, it has been reported to be associated with a few syndromes. A 9-year-old girl with minor thalassemia referred to the Department of Pediatric Dentistry of the Mashhad Faculty ...
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